Intra-hepatic portal-venous collaterals are characteristic of Budd-Chiari syndrome (BCS) and are usually of small caliber and seen on Doppler. Creation of large portal-systemic shunt, either radiologically (Transjugular intrahepatic porto-systemic shunt) or surgically results in excellent long term outcomes in BCS. Here, we report a series of three rare cases of asymptomatic BCS, who had spontaneous large intra-hepatic portal-systemic shunts.
Keywords: BCS, Budd–Chiari Syndrome; HE, Hepatic Encephalopathy; HV, Hepatic Vein; IVC, Inferior Vena Cava; LFT, Liver Function Test; MTHFR, Methylenetetrahydrofolate Reductase; PHT, Portal Hypertension; SIPSS, Spontaneous Intrahepatic Portosystemic venous shunt; TIPSS, Transjugular intrahepatic portosystemic shunt; anticoagulation therapy; hepatic vein outflow tract obstruction; transjugular intrahepatic portosystemic shunt.